TY - JOUR T1 - Mitochondrial disruption in peroxisome deficient cells is hepatocyte selective but is not mediated by common hepatic peroxisomal metabolites JF - Mitochondrion Y1 - 2018 A1 - Shinde, A.B. A1 - Baboota, R.K. A1 - Denis, S. A1 - Loizides-Mangold, U. A1 - Peeters, A. A1 - Espeel, M. A1 - Malheiro, A.R. A1 - Riezman, H. A1 - Vinckier, S. A1 - Vaz, F.M. A1 - Brites, P. A1 - Ferdinandusse, S. A1 - Van Veldhoven, P.P. A1 - Baes, M. VL - 39 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-85029209217&doi=10.1016%2fj.mito.2017.08.013&partnerID=40&md5=f181ab9ca63294b5280c4b088b12993c N1 - Export Date: 19 March 2018 ER - TY - JOUR T1 - The Dyslexia-susceptibility Protein KIAA0319 Inhibits Axon Growth Through Smad2 Signaling JF - Cerebral cortex (New York, N.Y. : 1991) Y1 - 2017 A1 - Franquinho, F. A1 - Nogueira-Rodrigues, J. A1 - Duarte, J.M. A1 - Esteves, S.S. A1 - Carter-Su, C. A1 - Monaco, A.P. A1 - Molnár, Z. A1 - Velayos-Baeza, A. A1 - Brites, P. A1 - Sousa, M.M. VL - 27 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-85021858395&doi=10.1093%2fcercor%2fbhx023&partnerID=40&md5=1fb6898fb1cd31cd4a3605e4a984adb5 IS - 3 N1 - Cited By :1Export Date: 19 March 2018 ER - TY - JOUR T1 - The Actin-Binding Protein α-Adducin Is Required for Maintaining Axon Diameter JF - Cell Reports Y1 - 2016 A1 - Leite, S.C. A1 - Sampaio, P. A1 - Sousa, V.F. A1 - Nogueira-Rodrigues, J. A1 - Pinto-Costa, R. A1 - Peters, L.L. A1 - Brites, P. A1 - Sousa, M.M. VL - 15 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-84962762309&doi=10.1016%2fj.celrep.2016.03.047&partnerID=40&md5=3e88204ff973b6a06592374958cdfa38 IS - 3 N1 - Cited By :9Export Date: 19 March 2018 ER - TY - JOUR T1 - Axonal pathology in Krabbe's disease: The cytoskeleton as an emerging therapeutic target JF - Journal of Neuroscience Research Y1 - 2016 A1 - Nogueira-Rodrigues, J. A1 - Brites, P. A1 - Sousa, M.M. VL - 94 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-84990185948&doi=10.1002%2fjnr.23771&partnerID=40&md5=107d641b8b9a5d522ad72cd700d72169 IS - 11 N1 - Cited By :1Export Date: 19 March 2018 ER - TY - JOUR T1 - Early-onset Purkinje cell dysfunction underlies cerebellar ataxia in peroxisomal multifunctional protein-2 deficiency JF - Neurobiology of Disease Y1 - 2016 A1 - De Munter, S. A1 - Verheijden, S. A1 - Vanderstuyft, E. A1 - Malheiro, A.R. A1 - Brites, P. A1 - Gall, D. A1 - Schiffmann, S.N. A1 - Baes, M. VL - 94 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-84976872223&doi=10.1016%2fj.nbd.2016.06.012&partnerID=40&md5=878da79db87e1583f0249d19f8d9e9a3 N1 - Cited By :1Export Date: 19 March 2018 ER - TY - JOUR T1 - Myelin Lipids Inhibit Axon Regeneration Following Spinal Cord Injury: a Novel Perspective for Therapy JF - Molecular Neurobiology Y1 - 2016 A1 - Mar, F.M. A1 - Da Silva, T.F. A1 - Morgado, M.M. A1 - Rodrigues, L.G. A1 - Rodrigues, D. A1 - Pereira, M.I.L. A1 - Marques, A. A1 - Sousa, V.F. A1 - Coentro, J. A1 - Sa-Miranda, C. A1 - Sousa, M.M. A1 - Brites, P. VL - 53 UR - https://www.scopus.com/inward/record.uri?eid=2-s2.0-84958225895&doi=10.1007%2fs12035-014-9072-3&partnerID=40&md5=42026944f8c340f73d21052e5318dc86 IS - 2 N1 - Cited By :3Export Date: 19 March 2018 ER - TY - JOUR T1 - Plasmalogen phospholipids protect internodal myelin from oxidative damage JF - Free Radical Biology and Medicine Y1 - 2015 A1 - Luoma, A.M. A1 - Kuo, F. A1 - Cakici, O. A1 - Crowther, M.N. A1 - Denninger, A.R. A1 - Avila, R.L. A1 - Brites, P. A1 - Kirschner, D.A. VL - 84 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-84929162848&partnerID=40&md5=70196bbfa77635ad3138b1fc4921ee50 N1 - Cited By :1Export Date: 12 January 2016 ER - TY - JOUR T1 - Early axonal loss accompanied by impaired endocytosis, abnormal axonal transport, and decreased microtubule stability occur in the model of Krabbe's disease JF - Neurobiology of Disease Y1 - 2014 A1 - Teixeira, C.A. A1 - Miranda, C.O. A1 - Sousa, V.F. A1 - Santos, T.E. A1 - Malheiro, A.R. A1 - Solomon, M. A1 - Maegawa, G.H. A1 - Brites, P. A1 - Sousa, M.M. VL - 66 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-84896968554&partnerID=40&md5=6c5b2620a1545e219d15478dec381dec N1 - Export Date: 25 June 2014 ER - TY - JOUR T1 - Peripheral nervous system plasmalogens regulate Schwann cell differentiation and myelination JF - Journal of Clinical Investigation Y1 - 2014 A1 - Da Silva, T.F. A1 - Eira, J. A1 - Lopes, A.T. A1 - Malheiro, A.R. A1 - Sousa, V. A1 - Luoma, A. A1 - Avila, R.L. A1 - Wanders, R.J.A. A1 - Just, W.W. A1 - Kirschner, D.A. A1 - Sousa, M.M. A1 - Brites, P. VL - 124 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-84902172153&partnerID=40&md5=f7824a8926ddb313c0a8e6141f216dd8 IS - 6 N1 - Export Date: 25 June 2014 ER - TY - JOUR T1 - Advances and pitfalls of cell therapy in metabolic leukodystrophies JF - Cell Transplantation Y1 - 2013 A1 - Miranda, C.O. A1 - Brites, P. A1 - Sousa, M.M. A1 - Teixeira, C.A. VL - 22 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-84874371497&partnerID=40&md5=ace99d300c754429313ccce0df7b484c IS - 2 N1 - Export Date: 18 March 2013Source: Scopus ER - TY - JOUR T1 - The importance of ether-phospholipids: A view from the perspective of mouse models JF - Biochimica et Biophysica Acta - Molecular Basis of Disease Y1 - 2012 A1 - Da Silva, T.F. A1 - Sousa, V.F. A1 - Malheiro, A.R. A1 - Brites, P. VL - 1822 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-84864039497&partnerID=40&md5=f4acf39f3b3e0418f6c555c99a5b5b43 IS - 9 N1 - Cited By (since 1996): 1Export Date: 18 March 2013Source: Scopus ER - TY - JOUR T1 - Alkyl-glycerol rescues plasmalogen levels and pathology of ether-phospholipid deficient mice JF - PLoS ONE Y1 - 2011 A1 - Brites, P. A1 - Ferreira, A.S. A1 - Da Silva, T.F. A1 - Sousa, V.F. A1 - Malheiro, A.R. A1 - Duran, M. A1 - Waterham, H.R. A1 - Baes, M. A1 - Wanders, R.J.A. VL - 6 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-82755170548&partnerID=40&md5=ee692b90c449e11127ff1250fd19f673 IS - 12 N1 - Cited By (since 1996): 5Export Date: 18 March 2013Source: ScopusArt. No.: e28539 ER - TY - JOUR T1 - Biosynthesis of ether-phospholipids including plasmalogens, peroxisomes and human disease: New insights into an old problem JF - Clinical Lipidology Y1 - 2010 A1 - Wanders, R.J. A1 - Brites, P. VL - 5 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-77953817755&partnerID=40&md5=95333a892fe4087ebad8d312f5961be4 IS - 3 N1 - Cited By (since 1996): 1Export Date: 18 March 2013Source: Scopus ER - TY - JOUR T1 - Peroxisomes, lipid metabolism and lipotoxicity JF - Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids Y1 - 2010 A1 - Wanders, R.J.A. A1 - Ferdinandusse, S. A1 - Brites, P. A1 - Kemp, S. VL - 1801 UR - http://www.scopus.com/inward/record.url?eid=2-s2.0-76349092667&partnerID=40&md5=af11b03a5bfdeefd41aa995c7d92bff3 IS - 3 N1 - Cited By (since 1996): 36Export Date: 18 March 2013Source: Scopus ER -